Seminar on pseudo-Hirschsprung's disease and related disorders.
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منابع مشابه
Health-related quality of life in children and adolescents undergoing surgery for Hirschsprung's disease and anorectal malformations.
PURPOSE The objective was to describe health related quality of life (HRQoL) after surgery for Hirschsprung's disease (HD) and anorectal malformations (ARMs) in children according to their own perception and that of their parents, by different age groups, the presence of functional disorders, and diet indication. METHODS This is a cross-sectional descriptive study. Participants were patients ...
متن کاملMegacolon in an adult case of hypoganglionosis, a pseudo-Hirschsprung's disease: an autopsy study.
We report an autopsied 20-year-old man case of intestinal necrosis associated with megacolon from hypoganglionosis, a pseudo-Hirschsprung's disease. The patient had suffered from severe constipation since two years of age, and presented abdominal distention from age ten. Autopsy revealed marked dilatation and necrosis of the entire large intestine. Although ganglion cells in the intestinal plex...
متن کاملDiagnostic Value of Calretinin and S100 Immunohistochemistry in Hirschsprung's Disease
Background Rectal biopsy and its histopathological study with hematoxylin and eosin (HE) is the gold standard for Hirschsprung's disease (HD) diagnosis. However, there are some limitations in the diagnosis of ganglion cells in HE approach. Recently, it was reported that the utility of Calretinin is a reliable ancillary immunohistochemistry (IHC) test for HD diagn...
متن کاملSuccessful redo pull-through for Hirschsprung's disease in a Haddad syndrome patient.
Haddad syndrome is characterized by congenital central hypoventilation syndrome (Ondine's curse) associated with segmental distal gut aganglionosis (Hirschsprung's disease). The prognosis of Haddad syndrome is very poor, and survival is often less than 2 years. Treatment of Hirschsprung's disease is usually influenced by the association with Ondine's curse. We report the case of a girl with Had...
متن کاملبررسی روایی نتایج روش برش انجمادی در مقایسه با روش برش‌های دائمی (روش استاندارد) در تشخیص بیماری هیرشپرونگ
Background and Objectives: Hirschsprung's disease is one of the congenital movement disorders of the bowel whose accurate and timely diagnosis in childhood is important. The disease occurs due to lack of ganglion cells in the distal part of the digestive system and leads to functional obstruction of the colon. Recently, by the frozen section method, the diagnosis and treatment of the disease is...
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عنوان ژورنال:
- Archives of disease in childhood
دوره 41 216 شماره
صفحات -
تاریخ انتشار 1966